Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Lys4Gln (p.K4Q) ( ENST00000549940.5, ENST00000299314.12, ENST00000392919.4, ENST00000549165.1 )
GNPTAB p.Lys4Gln (p.K4Q) ( ENST00000299314.12, ENST00000392919.4, ENST00000549165.1, ENST00000549940.5 )
Associated Disease
Pseudo-Hurler polydystrophy
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.10A>C (p.Lys4Gln) AND Pseudo-Hurler polydystrophy
ClinVar Allele ID
17813
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.10A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2006-03-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000002903
ClinVar Disease
Pseudo-Hurler polydystrophy
Observed Origin Sample
germline
Pubmed
16465621
Drugs