Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Trp894Ter (p.W894*) ( ENST00000299314.12 )
GNPTAB p.Trp894Ter (p.W894*) ( ENST00000299314.12 )
Associated Disease
Mucolipidosis type II
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.2681G>A (p.Trp894Ter) AND Mucolipidosis type II
ClinVar Allele ID
17806
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.2681G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2005-10-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000002895
ClinVar Disease
Mucolipidosis type II
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
16116615
Drugs