Annotation Detail

Information
Associated Genes
MEFV
Associated Variants
MEFV p.Glu148Gln (p.E148Q) ( ENST00000541159.5, ENST00000339854.8, ENST00000536379.5, ENST00000219596.6 )
MEFV p.Glu148Gln (p.E148Q) ( ENST00000219596.6, ENST00000339854.8, ENST00000536379.5, ENST00000541159.5 )
Associated Disease
familial Mediterranean fever
Source Database
ClinVar
Description
NM_000243.3(MEFV):c.442G>C (p.Glu148Gln) AND Familial Mediterranean fever
ClinVar Allele ID
17581
ClinVar RefSeq Alternation Syntax
NM_000243.3:c.442G>C
ClinVar RefSeq Alternation Syntax
NM_001198536.2:c.277+1685G>C
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2024-03-25
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000002651
ClinVar Disease
Familial Mediterranean fever
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
31204589
Pubmed
7677151
Pubmed
11903360
Pubmed
9668175
Pubmed
11464248
Pubmed
10090880
Drugs