Annotation Detail

Information
Associated Genes
ANO5
Associated Variants
ANO5 p.Arg758Cys (p.R758C) ( ENST00000683411.1, ENST00000682341.1, ENST00000683437.1, ENST00000683197.1, ENST00000682266.1, ENST00000324559.9, ENST00000684663.1 )
ANO5 p.Arg758Cys (p.R758C) ( ENST00000324559.9, ENST00000682266.1, ENST00000682341.1, ENST00000683197.1, ENST00000683411.1, ENST00000683437.1, ENST00000684663.1 )
Associated Disease
Miyoshi muscular dystrophy 3
Source Database
ClinVar
Description
NM_213599.3(ANO5):c.2272C>T (p.Arg758Cys) AND Miyoshi muscular dystrophy 3
ClinVar Allele ID
17205
ClinVar RefSeq Alternation Syntax
NM_001142649.2:c.2269C>T
ClinVar RefSeq Alternation Syntax
NM_213599.3:c.2272C>T
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2022-11-22
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000002250
ClinVar Disease
Miyoshi muscular dystrophy 3
Observed Origin Sample
germline
Observed Origin Sample
maternal
Observed Origin Sample
unknown
Pubmed
22402862
Pubmed
17132147
Pubmed
20096397
Drugs