Annotation Detail

Information
Associated Genes
OCA2
Associated Variants
OCA2 p.Ala481Thr (p.A481T) ( ENST00000354638.8, ENST00000353809.9 )
OCA2 p.Ala481Thr (p.A481T) ( ENST00000353809.9, ENST00000354638.8 )
Associated Disease
Tyrosinase-positive oculocutaneous albinism
Source Database
ClinVar
Description
NM_000275.3(OCA2):c.1441G>A (p.Ala481Thr) AND Tyrosinase-positive oculocutaneous albinism
ClinVar Allele ID
15993
ClinVar RefSeq Alternation Syntax
NM_000275.3:c.1441G>A
ClinVar RefSeq Alternation Syntax
NM_001300984.2:c.1369G>A
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2022-07-12
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000001005
ClinVar Disease
Tyrosinase-positive oculocutaneous albinism
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
17568986
Pubmed
12687678
Pubmed
8302318
Pubmed
8980282
Drugs