Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 c.7189+3A>C ( ENST00000691014.1, ENST00000356175.7, ENST00000687027.1, ENST00000693617.1, ENST00000358273.9, ENST00000696138.1, ENST00000684826.1 )
NF1 c.7189+3A>C ( ENST00000356175.7, ENST00000358273.9, ENST00000684826.1, ENST00000687027.1, ENST00000691014.1, ENST00000693617.1, ENST00000696138.1 )
Associated Disease
Neurofibromatosis, familial spinal
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.7189+3A>C AND Neurofibromatosis, familial spinal
ClinVar Allele ID
15408
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.7189+3A>C
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.7126+3A>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2000-01-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000400
ClinVar Disease
Neurofibromatosis, familial spinal
Observed Origin Sample
germline
Pubmed
10862084
Pubmed
1745350
Drugs