Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Gln1341Ter (p.Q1341*) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
NF1 p.Gln1341Ter (p.Q1341*) ( ENST00000356175.7, ENST00000358273.9, ENST00000691014.1, ENST00000696138.1 )
Associated Disease
Neurofibromatosis, type 1
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.4021C>T (p.Gln1341Ter) AND Neurofibromatosis, type 1
ClinVar Allele ID
15396
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.4021C>T
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.4021C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2023-10-03
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000385
ClinVar Disease
Neurofibromatosis, type 1
Observed Origin Sample
germline
Observed Origin Sample
somatic
Pubmed
10677298
Drugs