Annotation Detail

Information
Associated Genes
NF1
Associated Variants
NF1 p.Arg1970Ter (p.R1970*) ( ENST00000684826.1, ENST00000358273.9, ENST00000693617.1, ENST00000696138.1, ENST00000691014.1, ENST00000356175.7, ENST00000687027.1 )
NF1 p.Arg1970Ter (p.R1970*) ( ENST00000356175.7, ENST00000358273.9, ENST00000684826.1, ENST00000687027.1, ENST00000691014.1, ENST00000693617.1, ENST00000696138.1 )
Associated Disease
Neurofibromatosis, type 1
Source Database
ClinVar
Description
NM_001042492.3(NF1):c.5908A>T (p.Arg1970Ter) AND Neurofibromatosis, type 1
ClinVar Allele ID
15374
ClinVar RefSeq Alternation Syntax
NM_000267.3:c.5845A>T
ClinVar RefSeq Alternation Syntax
NM_001042492.3:c.5908A>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1994-04-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000363
ClinVar Disease
Neurofibromatosis, type 1
Observed Origin Sample
germline
Pubmed
1757093
Pubmed
8069310
Drugs