Annotation Detail

Information
Associated Genes
XPC
Associated Variants
XPC c.2033+2T>G ( ENST00000285021.12 )
XPC c.2033+2T>G ( ENST00000285021.12 )
Associated Disease
Xeroderma pigmentosum, group C
Source Database
ClinVar
Description
NM_004628.5(XPC):c.2033+2T>G AND Xeroderma pigmentosum, group C
ClinVar Allele ID
15296
ClinVar RefSeq Alternation Syntax
NM_001354726.2:c.1454+2T>G
ClinVar RefSeq Alternation Syntax
NM_004628.5:c.2033+2T>G
ClinVar RefSeq Alternation Syntax
NM_001354729.2:c.2015+2T>G
ClinVar RefSeq Alternation Syntax
NM_001354727.2:c.1872+1678T>G
ClinVar RefSeq Alternation Syntax
NM_001354730.2:c.1787+2T>G
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
1998-11-01
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000281
ClinVar Disease
Xeroderma pigmentosum, group C
Observed Origin Sample
germline
Pubmed
9804340
Drugs