Annotation Detail

Information
Associated Genes
XPC
Associated Variants
XPC p.Lys431ArgfsTer6 (p.K431Rfs*6) ( ENST00000285021.12 )
XPC p.Lys431ArgfsTer6 (p.K431Rfs*6) ( ENST00000285021.12 )
Associated Disease
Xeroderma pigmentosum, group C
Source Database
ClinVar
Description
NM_004628.5(XPC):c.1292_1293del (p.Lys431fs) AND Xeroderma pigmentosum, group C
ClinVar Allele ID
15295
ClinVar RefSeq Alternation Syntax
NR_148950.2:n.1325_1326del
ClinVar RefSeq Alternation Syntax
NM_001354726.2:c.713_714del
ClinVar RefSeq Alternation Syntax
NM_001354727.2:c.1292_1293del
ClinVar RefSeq Alternation Syntax
NM_001354729.2:c.1274_1275del
ClinVar RefSeq Alternation Syntax
NM_004628.5:c.1292_1293del
ClinVar RefSeq Alternation Syntax
NR_148951.2:n.1201_1202del
ClinVar RefSeq Alternation Syntax
NM_001354730.2:c.1292_1293del
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-05-17
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000000280
ClinVar Disease
Xeroderma pigmentosum, group C
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
8298653
Drugs