Annotation Detail

Information
Associated Genes
MLH1
Associated Variants
MLH1 p.Gly67Arg (p.G67R) ( ENST00000466900.6, ENST00000435176.5, ENST00000456676.7, ENST00000458205.6, ENST00000455445.6, ENST00000492474.6, ENST00000441265.6, ENST00000539477.6, ENST00000485889.2, ENST00000231790.8, ENST00000536378.5, ENST00000450420.6, ENST00000616768.6, ENST00000673673.2, ENST00000673715.1, ENST00000673899.1, ENST00000673990.2, ENST00000674019.1, ENST00000713802.1 )
MLH1 p.Gly67Arg (p.G67R) ( ENST00000231790.8, ENST00000435176.5, ENST00000441265.6, ENST00000450420.6, ENST00000455445.6, ENST00000456676.7, ENST00000458205.6, ENST00000466900.6, ENST00000485889.2, ENST00000492474.6, ENST00000536378.5, ENST00000539477.6, ENST00000616768.6, ENST00000673673.2, ENST00000673715.1, ENST00000673899.1, ENST00000673990.2, ENST00000674019.1, ENST00000713802.1 )
Associated Disease
Lynch syndrome
Source Database
CIViC Evidence
Description
This variant, identified in a case of microsatellite-unstable colorectal cancer was confirmed to be somatic in a patient with suspected Lynch Syndrome (LS). The patient was therefore negative for LS. However, based on this study we can infer that the variant would predispose to LS in a germline setting. Loss of heterozygosity of the wildtype allele was demonstrated.
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/1821
Gene URL
https://civic.genome.wustl.edu/links/genes/3532
Variant URL
https://civic.genome.wustl.edu/links/variants/757
Rating
2
Evidence Type
Predisposing
Disease
Lynch Syndrome
Evidence Direction
Supports
Evidence Level
E
Clinical Significance
Uncertain Significance
Pubmed
25111426
Drugs