Annotation Detail

Information
Associated Genes
CEBPA
Associated Variants
CEBPA MUTATION
CEBPA MUTATION
Associated Disease
acute myeloid leukemia
Source Database
CIViC Evidence
Description
In young patients (age 16-60) with previously untreated, cytogenetically normal acute myeloid leukemia, CEBPA mutation was significantly associated with complete remission in multivariate analysis (odds ratio, 1.33; 95% confidence interval [CI], 1.01 to 1.74). Multivariate analysis was performed on all patients that were evaluated for a mutation in at least 1 gene (CEBPA, FLT3-ITD or NPM1) totaling 693/872 patients in the study. Only 509 patients in the study were evaluated for CEBPA, 67 of which had a mutation.
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/167
Gene URL
https://civic.genome.wustl.edu/links/genes/15
Variant URL
https://civic.genome.wustl.edu/links/variants/29
Rating
4
Evidence Type
Prognostic
Disease
Acute Myeloid Leukemia
Evidence Direction
Supports
Evidence Level
B
Clinical Significance
Better Outcome
Pubmed
18450602
Drugs