Annotation Detail

Information
Associated Genes
ATRX
Associated Variants
ATRX UNDEREXPRESSION ( ENST00000373344.11 )
ATRX UNDEREXPRESSION ( ENST00000373344.11 )
Associated Disease
glioblastoma
Source Database
CIViC Evidence
Description
In a glioblastoma mouse model induced by NRAS and p53 knockdown, ATRX loss was associated with a decreased median survival (69 days vs. 84 days; P = .0032). Also, the tumors grew to a larger size at earlier time points. ATRX loss was also associated with greater microsatellite instability.
Variant Origin
N/A
Variant Origin
N/A
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/1648
Gene URL
https://civic.genome.wustl.edu/links/genes/525
Variant URL
https://civic.genome.wustl.edu/links/variants/648
Rating
4
Evidence Type
Prognostic
Disease
Glioblastoma Multiforme
Evidence Direction
Supports
Evidence Level
D
Clinical Significance
Poor Outcome
Pubmed
26936505
Drugs