Annotation Detail

Information
Associated Genes
ATM
Associated Variants
ATM UNDEREXPRESSION ( ENST00000278616.10 )
ATM UNDEREXPRESSION ( ENST00000278616.10 )
Associated Disease
chronic lymphocytic leukemia
Source Database
CIViC Evidence
Description
43 B-CLL patients with LoH or reduced protein levels (<50% normal expression, radioimmunoassay, western blot) of ATM were found to have significantly shorter overall survival (35.6 vs. 97.3 months; P=0.003) when compared to 108 patients with normal expression levels.
Variant Origin
N/A
Variant Origin
N/A
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/1564
Gene URL
https://civic.genome.wustl.edu/links/genes/69
Variant URL
https://civic.genome.wustl.edu/links/variants/179
Rating
3
Evidence Type
Prognostic
Disease
Chronic Lymphocytic Leukemia
Evidence Direction
Supports
Evidence Level
B
Clinical Significance
Poor Outcome
Pubmed
9788599
Drugs