Annotation Detail

Information
Associated Genes
KDR
Associated Variants
KDR p.Asp717Val (p.D717V) ( ENST00000263923.5 )
KDR p.Asp717Val (p.D717V) ( ENST00000263923.5 )
Associated Disease
angiosarcoma
Source Database
CIViC Evidence
Description
COS-7 cells were transiently transfected with expression constructs encoding cDNAs for wild-type or D717V-mutant KDR. Autophosphorylation was observed on tyrosine of mutant cells, but not wild-type cells, which were starved from serum for 6 hours without rhVEGF stimulation. Decreased phosphorylation in mutant cells was noted after treatment with either sunitinib or sorafenib.
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/1107
Gene URL
https://civic.genome.wustl.edu/links/genes/3153
Variant URL
https://civic.genome.wustl.edu/links/variants/468
Rating
3
Evidence Type
Predictive
Disease
Angiosarcoma
Evidence Direction
Supports
Drug
Sunitinib,Sorafenib
Evidence Level
D
Clinical Significance
Sensitivity/Response
Pubmed
19723655
Drugs
Drug NameSensitivitySupported
SorafenibSensitivitytrue
SunitinibSensitivitytrue