Annotation Detail

Information
Associated Genes
EGFR
Associated Variants
EGFR p.Pro753Ser (p.P753S) ( ENST00000275493.7, ENST00000450046.2, ENST00000455089.5 )
EGFR p.Pro753Ser (p.P753S) ( ENST00000450046.2, ENST00000275493.7, ENST00000455089.5 )
Associated Disease
skin squamous cell carcinoma
Source Database
CIViC Evidence
Description
72-year old male patient presents with SCC with a mutation profile consistent with UV exposure. Sequencing revealed a number of abnormalities including P753S mutation in EGFR. Patient began therapy with cetuximab and sirolimus and continued for 9 months. Disease burden was not measurable by Response Evaluation Criteria in Solid Tumors.
Variant Origin
somatic
Variant Origin
Somatic
Evidence URL
https://civic.genome.wustl.edu/links/evidence_items/1089
Gene URL
https://civic.genome.wustl.edu/links/genes/19
Variant URL
https://civic.genome.wustl.edu/links/variants/460
Rating
3
Evidence Type
Predictive
Disease
Skin Squamous Cell Carcinoma
Evidence Direction
Supports
Drug
Cetuximab,Sirolimus
Evidence Level
C
Clinical Significance
Sensitivity/Response
Pubmed
24934779
Drugs
Drug NameSensitivitySupported
CetuximabSensitivitytrue
SirolimusSensitivitytrue