chrX:100652441:> Detail (hg19)
Information
Genome
Assembly | Position |
---|---|
hg19 | chrX:100,652,441-100,662,913 |
hg38 | chrX:101,397,453-101,407,925 |
HGVS
Type | Transcript | Protein |
---|---|---|
Summary
MGeND
Clinical significance | |
Variant entry | |
GWAS entry | |
Disease area statistics | Show details |
Frequency
[No Data.]
Prediction
[No Data.]
ClinVar
Clinical Significance | |
Review star | [No Data.] |
Show details |
Links
Disease area statistics
[No Data.]
MGeND
[No Data.]
ClinVar
[No Data.]
CIViC
[No Data.]
DisGeNET
Score | Disease name | Description | Source | Pubmed | Links |
---|---|---|---|---|---|
0.001 | hypertrophic cardiomyopathy | NA | BeFree | Detail | |
<0.001 | corneal dystrophy | NA | BeFree | Detail | |
0.002 | Exanthema | NA | BeFree | Detail | |
<0.001 | glaucoma | NA | BeFree | Detail | |
<0.001 | Glycogen storage disease type II | We tested several compounds in order to identify novel small molecules that prev... | BeFree | 25409744 | Detail |
<0.001 | Hypertensive disease | NA | BeFree | Detail | |
<0.001 | influenza | NA | BeFree | Detail | |
0.001 | Kidney Diseases | NA | BeFree | Detail | |
0.001 | Kidney Failure, Chronic | NA | BeFree | Detail | |
<0.001 | Lung diseases | NA | BeFree | Detail | |
0.001 | Metabolic Diseases | NA | BeFree | Detail | |
0.001 | Inborn errors of metabolism | NA | BeFree | Detail | |
<0.001 | Neuralgia | The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalges... | BeFree | 25337704 | Detail |
<0.001 | familial Mediterranean fever | NA | BeFree | Detail | |
<0.001 | pseudoxanthoma elasticum | NA | BeFree | Detail | |
0.001 | kidney failure | Fabry disease results from deficient α-galactosidase A activity and globotriaosy... | BeFree | 25795794 | Detail |
0.005 | Cerebrovascular accident | NA | BeFree,GAD | Detail | |
0.010 | Lysosomal Storage Diseases | Screening for Fabry disease (FD), an X-linked lysosomal storage disorder, reveal... | BeFree | 25187469 | Detail |
0.010 | Lysosomal Storage Diseases | Fabry disease (FD) is an X-linked lysosomal storage disorder resulting from defi... | BeFree | 25468650 | Detail |
0.010 | Lysosomal Storage Diseases | Fabry disease is an X-linked lysosomal storage disease due to deficient α-galact... | BeFree | 25542581 | Detail |
0.010 | Lysosomal Storage Diseases | Fabry disease is an X-linked lysosomal storage disease caused by deficient activ... | BeFree | 25553976 | Detail |
0.010 | Lysosomal Storage Diseases | Fabry disease (FD) is a lysosomal storage disorder associated with loss of activ... | BeFree | 26046974 | Detail |
0.001 | Left Ventricular Hypertrophy | We developed a diagnostic algorithm for adults with LVH (maximal wall thickness ... | BeFree | 25442977 | Detail |
<0.001 | neurological pain | NA | BeFree | Detail | |
<0.001 | Thrombosis of cerebral veins | NA | BeFree | Detail | |
<0.001 | X-linked agammaglobulinemia | NA | BeFree | Detail | |
<0.001 | Acroparesthesia | NA | BeFree | Detail | |
<0.001 | Papillary thyroid carcinoma | NA | BeFree | Detail | |
0.665 | Fabry disease | Newborn screening for Fabry disease in Taiwan reveals a high incidence of the la... | UNIPROT | 19621417 | Detail |
0.665 | Fabry disease | Two novel mutations (L32P) and (G85N) among five different missense mutations in... | UNIPROT | 7599642 | Detail |
0.665 | Fabry disease | Nature and frequency of mutations in the alpha-galactosidase A gene that cause F... | UNIPROT | 7504405 | Detail |
0.665 | Fabry disease | NA | UNIPROT | Detail | |
0.665 | Fabry disease | Fabry disease: twenty-two novel mutations in the alpha-galactosidase A gene and ... | UNIPROT | 10916280 | Detail |
0.665 | Fabry disease | Fabry disease: identification of novel alpha-galactosidase A mutations and molec... | UNIPROT | 10208848 | Detail |
<0.001 | Generalized glycogen storage disease of infants | We tested several compounds in order to identify novel small molecules that prev... | BeFree | 25409744 | Detail |
<0.001 | Hyperalgesia, Thermal | The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalges... | BeFree | 25337704 | Detail |
0.002 | Spots on skin | NA | BeFree | Detail | |
<0.001 | Endothelial dysfunction | NA | BeFree | Detail | |
0.001 | Cardiomyopathies | NA | BeFree | Detail | |
<0.001 | Ischemic stroke | NA | BeFree | Detail | |
<0.001 | Congenital ectopia | NA | BeFree | Detail | |
<0.001 | Renal Insufficiency | Fabry disease results from deficient α-galactosidase A activity and globotriaosy... | BeFree | 25795794 | Detail |
<0.001 | Cornea verticillata | NA | BeFree | Detail | |
0.001 | Chronic kidney disease stage 5 | NA | BeFree | Detail | |
<0.001 | Mechanical Allodynia | The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalges... | BeFree | 25337704 | Detail |
<0.001 | Ischemic Cerebrovascular Accident | NA | BeFree | Detail | |
<0.001 | Small fiber neuropathy | Taken together, our findings imply that the α-GalA KO mouse is a good model in w... | BeFree | 25337704 | Detail |
<0.001 | Small fiber neuropathy | Cryptogenic stroke and small fiber neuropathy of unknown etiology in patients wi... | BeFree | 25423912 | Detail |
<0.001 | granulomatosis with polyangiitis | He was diagnosed with Fabry's disease accompanying granulomatosis with polyangii... | BeFree | 25270872 | Detail |
0.120 | angiokeratoma | NA | BeFree,CTD_human | Detail | |
0.665 | Fabry disease | Fabry disease (FD) is an X-linked disease in which mutations of the GLA gene res... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 24645664 | Detail |
0.665 | Fabry disease | In adults with chronic kidney disease, an α-galactosidase A gene variant and an ... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25187469 | Detail |
0.665 | Fabry disease | He was diagnosed with Fabry's disease accompanying granulomatosis with polyangii... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25270872 | Detail |
0.665 | Fabry disease | A family with various symptomatology suggestive of Anderson-Fabry disease and a ... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25281798 | Detail |
0.665 | Fabry disease | A heterozygous female with Fabry disease due to a novel α-galactosidase A mutati... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25295576 | Detail |
0.665 | Fabry disease | Taken together, our findings imply that the α-GalA KO mouse is a good model in w... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25337704 | Detail |
0.665 | Fabry disease | Molecular damage in Fabry disease: characterization and prediction of alpha-gala... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25382311 | Detail |
0.665 | Fabry disease | We tested several compounds in order to identify novel small molecules that prev... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25409744 | Detail |
0.665 | Fabry disease | Fabry disease (FD) is a multisystemic disorder with typical neurological manifes... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25423912 | Detail |
0.665 | Fabry disease | In adults with unexplained LVH and a GLA GVUS, severe LVH at young age and low v... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25442977 | Detail |
0.665 | Fabry disease | Our evidence shows that fibroblasts secrete minimal amounts of GLA and consequen... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25468650 | Detail |
0.665 | Fabry disease | The alpha-galactosidase A p.Arg118Cys variant does not cause a Fabry disease phe... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25468652 | Detail |
0.665 | Fabry disease | Fabry disease: renal sphingolipid distribution in the α-Gal A knockout mouse mod... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25542581 | Detail |
0.665 | Fabry disease | α-Galactosidase A knockout mice: progressive organ pathology resembles the type ... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25553976 | Detail |
0.665 | Fabry disease | GLA variants can lead to classical FD, an attenuated non-classical phenotype, or... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25596309 | Detail |
0.665 | Fabry disease | Anderson-Fabry Disease (AFD) is an X linked lysosomal storage disorder caused by... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25655062 | Detail |
0.665 | Fabry disease | Consequently, information on ocular findings and α-galactosidase A gene mutation... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 25781336 | Detail |
0.665 | Fabry disease | In addition to accumulation of α-galactosidase A substrates, other mechanisms ma... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 26046974 | Detail |
0.665 | Fabry disease | Here, we demonstrate the ability of solid lipid nanoparticle-based non-viral vec... | BeFree,CLINVAR,CTD_human,GAD,LHGDN,MGD,ORPHANET,UNIPROT | 26307832 | Detail |
<0.001 | brucellosis | NA | BeFree | Detail |
Annotation
Annotations
Descrption | Source | Links |
---|---|---|
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
We tested several compounds in order to identify novel small molecules that prevent premature degrad... | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalgesia and mechanical al... | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
Fabry disease results from deficient α-galactosidase A activity and globotriaosylceramide accumulati... | DisGeNET | Detail |
NA | DisGeNET | Detail |
Screening for Fabry disease (FD), an X-linked lysosomal storage disorder, reveals a significant numb... | DisGeNET | Detail |
Fabry disease (FD) is an X-linked lysosomal storage disorder resulting from deficiency of α-galactos... | DisGeNET | Detail |
Fabry disease is an X-linked lysosomal storage disease due to deficient α-galactosidase A (α-Gal A) ... | DisGeNET | Detail |
Fabry disease is an X-linked lysosomal storage disease caused by deficient activity of α-galactosida... | DisGeNET | Detail |
Fabry disease (FD) is a lysosomal storage disorder associated with loss of activity of the enzyme α-... | DisGeNET | Detail |
We developed a diagnostic algorithm for adults with LVH (maximal wall thickness (MWT) of >12 mm), GL... | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
Newborn screening for Fabry disease in Taiwan reveals a high incidence of the later-onset GLA mutati... | DisGeNET | Detail |
Two novel mutations (L32P) and (G85N) among five different missense mutations in six Danish families... | DisGeNET | Detail |
Nature and frequency of mutations in the alpha-galactosidase A gene that cause Fabry disease. | DisGeNET | Detail |
NA | DisGeNET | Detail |
Fabry disease: twenty-two novel mutations in the alpha-galactosidase A gene and genotype/phenotype c... | DisGeNET | Detail |
Fabry disease: identification of novel alpha-galactosidase A mutations and molecular carrier detecti... | DisGeNET | Detail |
We tested several compounds in order to identify novel small molecules that prevent premature degrad... | DisGeNET | Detail |
The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalgesia and mechanical al... | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
Fabry disease results from deficient α-galactosidase A activity and globotriaosylceramide accumulati... | DisGeNET | Detail |
NA | DisGeNET | Detail |
NA | DisGeNET | Detail |
The α-GalA null mice display neuropathic pain as evidenced by thermal hyperalgesia and mechanical al... | DisGeNET | Detail |
NA | DisGeNET | Detail |
Taken together, our findings imply that the α-GalA KO mouse is a good model in which to study the pe... | DisGeNET | Detail |
Cryptogenic stroke and small fiber neuropathy of unknown etiology in patients with alpha-galactosida... | DisGeNET | Detail |
He was diagnosed with Fabry's disease accompanying granulomatosis with polyangiitis on the basis of ... | DisGeNET | Detail |
NA | DisGeNET | Detail |
Fabry disease (FD) is an X-linked disease in which mutations of the GLA gene result in a deficiency ... | DisGeNET | Detail |
In adults with chronic kidney disease, an α-galactosidase A gene variant and an uncertain diagnosis ... | DisGeNET | Detail |
He was diagnosed with Fabry's disease accompanying granulomatosis with polyangiitis on the basis of ... | DisGeNET | Detail |
A family with various symptomatology suggestive of Anderson-Fabry disease and a genetic polymorphism... | DisGeNET | Detail |
A heterozygous female with Fabry disease due to a novel α-galactosidase A mutation exhibits a unique... | DisGeNET | Detail |
Taken together, our findings imply that the α-GalA KO mouse is a good model in which to study the pe... | DisGeNET | Detail |
Molecular damage in Fabry disease: characterization and prediction of alpha-galactosidase A patholog... | DisGeNET | Detail |
We tested several compounds in order to identify novel small molecules that prevent premature degrad... | DisGeNET | Detail |
Fabry disease (FD) is a multisystemic disorder with typical neurological manifestations such as stro... | DisGeNET | Detail |
In adults with unexplained LVH and a GLA GVUS, severe LVH at young age and low voltages on ECG exclu... | DisGeNET | Detail |
Our evidence shows that fibroblasts secrete minimal amounts of GLA and consequently normal fibroblas... | DisGeNET | Detail |
The alpha-galactosidase A p.Arg118Cys variant does not cause a Fabry disease phenotype: data from in... | DisGeNET | Detail |
Fabry disease: renal sphingolipid distribution in the α-Gal A knockout mouse model by mass spectrome... | DisGeNET | Detail |
α-Galactosidase A knockout mice: progressive organ pathology resembles the type 2 later-onset phenot... | DisGeNET | Detail |
GLA variants can lead to classical FD, an attenuated non-classical phenotype, or no disease at all. | DisGeNET | Detail |
Anderson-Fabry Disease (AFD) is an X linked lysosomal storage disorder caused by mutations in the α-... | DisGeNET | Detail |
Consequently, information on ocular findings and α-galactosidase A gene mutation may help assess the... | DisGeNET | Detail |
In addition to accumulation of α-galactosidase A substrates, other mechanisms may be involved in FD ... | DisGeNET | Detail |
Here, we demonstrate the ability of solid lipid nanoparticle-based non-viral vectors to increase the... | DisGeNET | Detail |
NA | DisGeNET | Detail |
Overlapped Transcript Coordinates
Gene | Transcript ID | Exon Number | Chromosome | Start | Stop | Type | Amino Mutation | Transcript Position | Links |
---|
Overlapped Transcript
Gene | Transcript ID | Chromosome | Start | Stop | Links |
---|
- Gene
- -
- dbSNP
- rs28935191 dbSNP
- Genome
- hg19
- Position
- chrX:100,652,441-100,662,913
- Variant Type
- snv
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