Annotation Detail

Information
Associated Genes
GLA
Associated Variants
GLA MUTATION
GLA MUTATION
Associated Disease
Lysosomal Storage Diseases
Source Database
DisGeNET
Description
Fabry disease is an X-linked lysosomal storage disease due to deficient α-galactosidase A (α-Gal A) activity and the resultant lysosomal accumulation of globotriaosylceramide (Gb3) and related lipids primarily in blood vessels, kidney, heart, and other organs.
Pubmed
25542581
Section of the abstract supporting the evidence
ALL_TEXT_1/3
Number of the section of the abstract supporting the evidence
1
Number of the sentence supporting the evidence
1
Original source reporting the Gene Disease association
BeFree
DisGENET score for the Gene Disease association
0.0100433492669712
Drugs