Annotation Detail

Information
Associated Genes
PCSK9
Associated Variants
PCSK9 p.Cys679= (p.C679=) ( ENST00000302118.5, ENST00000713786.1, ENST00000673903.1, ENST00000710286.1 )
PCSK9 p.Cys679= (p.C679=) ( ENST00000302118.5, ENST00000673903.1, ENST00000710286.1, ENST00000713786.1 )
Associated Disease
Hypercholesterolemia, autosomal dominant, 3
Source Database
ClinVar
Description
NM_174936.4(PCSK9):c.2037C>T (p.Cys679=) AND Hypercholesterolemia, autosomal dominant, 3
ClinVar Allele ID
3039309
ClinVar RefSeq Alternation Syntax
NR_176323.1:n.2149C>T
ClinVar RefSeq Alternation Syntax
NR_176319.1:n.2596C>T
ClinVar RefSeq Alternation Syntax
NM_001407245.1:c.1845C>T
ClinVar RefSeq Alternation Syntax
NM_001407241.1:c.2079C>T
ClinVar RefSeq Alternation Syntax
NR_176318.1:n.2121C>T
ClinVar RefSeq Alternation Syntax
NM_001407244.1:c.1863C>T
ClinVar RefSeq Alternation Syntax
NM_001407242.1:c.2040C>T
ClinVar RefSeq Alternation Syntax
NM_001407247.1:c.1536C>T
ClinVar RefSeq Alternation Syntax
NM_001407246.1:c.1662C>T
ClinVar RefSeq Alternation Syntax
NM_174936.4:c.2037C>T
ClinVar RefSeq Alternation Syntax
NR_176321.1:n.2275C>T
ClinVar RefSeq Alternation Syntax
NM_001407240.1:c.2160C>T
ClinVar RefSeq Alternation Syntax
NR_110451.3:n.2318C>T
ClinVar RefSeq Alternation Syntax
NR_176320.1:n.2560C>T
ClinVar RefSeq Alternation Syntax
NR_176322.1:n.2230C>T
ClinVar RefSeq Alternation Syntax
NM_001407243.1:c.1980C>T
ClinVar RefSeq Alternation Syntax
NR_176324.1:n.2537C>T
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2023-10-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003606599
ClinVar Disease
Hypercholesterolemia, autosomal dominant, 3
Observed Origin Sample
germline
Drugs