Annotation Detail

Information
Associated Genes
F11
Associated Variants
F11 p.Cys56Arg (p.C56R) ( ENST00000403665.7, ENST00000492972.6 )
F11 p.Cys56Arg (p.C56R) ( ENST00000403665.7, ENST00000492972.6 )
Associated Disease
Hereditary factor XI deficiency disease
Source Database
ClinVar
Description
NM_000128.4(F11):c.166T>C (p.Cys56Arg) AND Hereditary factor XI deficiency disease
ClinVar Allele ID
26940
ClinVar RefSeq Alternation Syntax
NM_001354804.2:c.166T>C
ClinVar RefSeq Alternation Syntax
NM_000128.4:c.166T>C
Clinical Significance Description
Pathogenic/Likely pathogenic
Clinical Significance Last Update
2022-06-30
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV000012676
ClinVar Disease
Hereditary factor XI deficiency disease
Observed Origin Sample
germline
Observed Origin Sample
unknown
Pubmed
11895778
Pubmed
10444286
Drugs